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Potter's Syndrome is a rare condition occurring in sporadic and autosomally recessive forms. It is incompatible with life.
The key problem is bilateral renal agenesis. Potter found this in 1 in 4000 births, especially males. Renal agenesis causes oligohydramnios.
The lack of amniotic fluid to cushion the fetus results in the characteristic squashed facies and other features of Potter's syndrome.