extrarenal manifestations

Last reviewed 07/2018

Cysts may occur in the liver, pancreas, spleen and lungs.

Hepatic cysts occur in 75% of patients over the age of 60 years. They appear to be affected by female steroid hormones, and, although they may occur in both sexes, massive cysts occur almost exclusively in women.

Non-cystic manifestations include:

  • increased incidence of mitral valve prolapse
  • intracranial berry aneurysms - in up to 40% of cases
  • increased frequency of colonic diverticula