This site is intended for healthcare professionals

Go to /sign-in page

You can view 5 more pages without signing in

Nonbullous congenital ichthyosis erythroderma

Last reviewed dd mmm yyyy. Last edited dd mmm yyyy

Authoring team

  • autosomal recessive inheritance
  • incidence of 1 in 300,000
  • generally presents as a 'colloidon baby' - this is followed by generalised erythroderma and scaling
  • the scale in this condition is grey or white; it is light and semi-adherant
  • severe disease may be complicated by fissures on the palms and soles of the feet, partial scarring alopecia and digital contractures
  • ectropions of the eyelids may persist into adult life and can result in exposure keratitis
  • sweating is generally reduced or absent; therefore care is required in avoiding hyperpyrexia
  • the genetic mutation causing this condition is, at present, unknown

Related pages

Create an account to add page annotations

Annotations allow you to add information to this page that would be handy to have on hand during a consultation. E.g. a website or number. This information will always show when you visit this page.