This site is intended for healthcare professionals

2428 pages added, reviewed or updated during the last month (last updated: 23/4/2021)

2428 pages added, reviewed or updated during the last month (last updated: 23/4/2021)


Medical search

treatment

FREE subscriptions for doctors and students... click here
You have 3 more open access pages.

Treatment is essentially surgical although the paroxysmal hypercyanotic attacks must be managed appropriately.

Surgery is often in two stages with a palliative procedure to improve symptoms followed later by a total repair:

  • palliative surgery involves creating a shunt between the aorta and pulmonary artery so that sufficient blood can enter the lungs. In a Blalock operation the subclavian artery is joined to the pulmonary artery and in a Waterston operation the ascending aorta is joined to the right pulmonary artery. Alternatively pulmonary valvotomy and infundibular resection may give relief in the Brock operation

  • total repair is undertaken as the child approaches school age

  • the use of an implantable cardioverter defibrillator should be considered following repair (1)

Reference:

  • 1) NICE (September 2000). Implantable cardioverter defibrillators for arrhythmias.

Last reviewed 10/2020

Links: