This site is intended for healthcare professionals

Go to /sign-in page

You can view 5 more pages before signing in

Extrahepatic biliary atresia

Last reviewed dd mmm yyyy. Last edited dd mmm yyyy

Authoring team

Biliary atresia is a congenitally acquired condition in which the biliary tree become progressively sclerosed and occluded. The main intrahepatic ducts become obliterated and death occurs in 98% of individuals by two years old if untreated.

The cause may be a congenital or perinatal infection, for example with reoviruses.

It occurs approximately once in 15 000 live births in the UK (1)

  • more common in females
  • more common in Asians

Approximately 20% of patients have other congenital abnormalities (2).


  • Kelly DA, Davenport M; Current management of biliary atresia. Arch Dis Child. 2007 Dec;92(12):1132-5.
  • Hartley JL, Davenport M, Kelly DA; Biliary atresia. Lancet. 2009 Nov 14;374(9702):1704-13.

Related pages

Create an account to add page annotations

Add information to this page that would be handy to have on hand during a consultation, such as a web address or phone number. This information will always be displayed when you visit this page