Aetiological classification of pulmonary fibrosis
Congenital causes:
- neurofibromatosis
- Gaucher's disease
- Niemann-Pick disease
- tuberous sclerosis
Chemical or dust inhalation:
- organic dusts e.g. moulds, avian proteins
- mineral dusts e.g. silica, coal dust, asbestos
- chemicals e.g. chlorine, nitrogen dioxide
Unknown causes:
- cryptogenic fibrosing alveolitis
- idiopathic haemosiderosis
- histiocytosis X
- sarcoidosis
Drugs:
- bleomycin, cyclophosphamide, methotrexate, hydralazine, busulphan, amiodarone
Iatrogenic and poisoning:
- radiation pneumonitis
- oxygen toxicity
- paraquat poisoning
Pulmonary involvement in other disease:
- rheumatoid arthritis
- ankylosing spondylitis
- Sjogren's syndrome
- systemic sclerosis
- dermatomyositis
Related pages
- Neurofibromatosis
- Gaucher's disease (GD)
- Niemann-Pick disease
- Tuberous sclerosis
- Cryptogenic fibrosing alveolitis
- Idiopathic pulmonary haemosiderosis
- Histiocytosis X
- Sarcoidosis
- Cyclophosphamide
- Methotrexate
- Hydralazine
- Busulphan
- Amiodarone
- Paraquat poisoning
- Rheumatoid arthritis
- Ankylosing spondylitis (AS)
- Sjogren's syndrome
- Systemic sclerosis
- Polymyositis and dermatomyositis
- Cyclin-dependent kinase 4 and 6 inhibitors (CDK4/6 inhibitors) (abemaciclib , palbociclib , ribociclib) and interstitial lung disease and pneumonitis
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