Potter's Syndrome is a rare condition occurring in sporadic and autosomally recessive forms. It is incompatible with life.
The key problem is bilateral renal agenesis. Potter found this in 1 in 4000 births, especially males. Renal agenesis causes oligohydramnios.
The lack of amniotic fluid to cushion the fetus results in the characteristic squashed facies and other features of Potter's syndrome.
Last reviewed 01/2018