This site is intended for healthcare professionals

Go to /sign-in page

You can view 5 more pages before signing in


Last reviewed dd mmm yyyy. Last edited dd mmm yyyy

Authoring team

Caroli disease and choledochal cysts have been associated with this disorder. In about 75% of patients there is also concomitant renal disease, for example renal tubular ectasia, nephronophthisis, or childhood polycystic disease.

Related pages

Create an account to add page annotations

Add information to this page that would be handy to have on hand during a consultation, such as a web address or phone number. This information will always be displayed when you visit this page